Heteroplasmy analysis in the Polish patients with 11778A mutation responsible for Leber hereditary optic neuropathy.

نویسندگان

  • Katarzyna Mroczek-Tońska
  • Dorota Ratajska
  • Cecile Guillot
  • Maria Sasiadek
  • Anna Ambroziak
  • Leszek Lubos
  • Ewa Bartnik
چکیده

We have analysed the heteroplasmy level in 11 individuals from 3 families harbouring the mitochondrial 11778A mutation responsible for Leber hereditary optic neuropathy using last cycle hot PCR. The mutation level exceeded 90% both in affected and in unaffected individuals. We also checked whether any of the families belonged to the J haplogroup of mitochondrial DNA and obtained a negative result.

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The Decrease in Mitochondrial DNA Mutation Load Parallels Visual Recovery in a Leber Hereditary Optic Neuropathy Patient

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عنوان ژورنال:
  • Acta biochimica Polonica

دوره 49 1  شماره 

صفحات  -

تاریخ انتشار 2002